A vestibular approach was used to remove the tissue and histopathological picture of the 4 patients showed loosely arranged curvilinear trabeculae with fibrous elements leading to a diagnosis of fibrous dysplasia. The involvement of the craniofacial skeleton is not uncommon and, generally, produces facial asymmetries. The craniofacial bones are involved in about 10% of subjects. Fibrous dysplasia of the skull and its differential. Cefalea, cornete medio, displasia fibrosa, cefalea rinogenica. Rbcp surgical approach to the treatment of craniofacial. The roentgenographic appearance in the cranial bones ranges from small, simple translucent areas to massive, sclerotic overgrowth.
The fibrous dysplasia is a benign bone disease, of slow growth and unknown etiology. Fd occurs in monostotic or polyostotic forms, and the latter may be associated with mccunealbright syndrome, which is the most severe form of polyostotic fd. Abstract fibrous dysplasia of bone fibrous dysplasia of bone is a noninherited developmental anomaly of bone characterized by abnormal proliferation of fibroblasts and differentiation of osteoblasts that cause a replacement of trabeculous bone by fibrous connective tissue. Fd can affect one bone monostotic form or multiple bones polyostotic form.
Consultation with an otolaryngologist may be necessary for persistent congestion and chronic sinus infections. A displasia fibrosa e uma lesao ossea com etiologia ainda desconhecida. It is mainly located in the maxillary bone, while its nasal. Pdf craniofacial fibrous dysplasia addressed through the. Tomografia computadorizada dos seios da face no plano axial. Nasal disorders fibrous dysplasia middle turbinate. A displasia fibrosa e classificado como doencas tumorais pode ser local ou generalizada, atingindo um ou mais ossos. Fibrous dysplasia fd is a nonneoplastic tumorlike congenital process, manifested as a localized defect in osteoblastic differentiation and maturation, with the replacement of normal bone with large fibrous stroma and islands of immature woven bone.
Fibrous dysplasia is an idiopathic benign disorder that is most frequent in young adults. Seram 2014 s12 anatomia y patologia tumoral benigna. Abstract headache is one of the most frequent symptoms in medicine that can be classified as primary, like tensional headache and migraine or secondary as in tumors, infections, or other causes. Fibrous dysplasia of middle turbinate associated with widal syndrome. Fibrous dysplasia has a varied radiographic appearance. A displasia fibrosa e uma alteracao fibroossea benig. Displasia fibrosa craneofacial avanzada por remodelacion. Fibrous dysplasia is a disorder where normal bone and marrow is replaced with fibrous tissue, resulting in formation of bone that is weak and prone to expansion. This lesion seems to originate from the nasal turbinates and paranasal sinus walls at the right side. The patient was forwarded to the surgical center for the lesion biopsy.
It is located mainly in the maxillary bone, affecting with certain frequency the perinasal cavities. Displasia fibrosa causas, sintomas, diagnostico e tratamento. Findings in a 25 yearold male consistent with fibrous dysplasia. May 24, 2012 the management of sinus and nasal congestion includes nasal saline spray, nasal steroid spray, antihistamines for those with seasonal allergies, and antibiotics for suspected bacterial sinus infections. Usually asymptomatic, its treatment is surgical when it creates an important facial. The aim of this study was to report a case of unilateral fibrous dysplasia in the maxilla, in the palate region, by using computed tomography. Summary osteofibrous displasia is an infrequent benign tumor in head and neck. As a result, most complications result from fracture, deformity, functional impairment, and pain.
Caracteristicas tomograficas da displasia fibrosa craniofacial. O principal diagnostico diferencial da forma monostotica, no envolvimento. Craniofacial fibrous dysplasia addressed through the intraoral and nasal access. Displasia fibrosa genetic and rare diseases information. The skull is a frequent site of the pathologic process now known as fibrous dysplasia and the skull changes are often the only manifestation of the disease. Displasia fibrosa diagnostico y tratamiento mayo clinic. In this article we report the case of a patient with fibrous dysplasia occupying the entire left maxillary sinus.
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